Heterotaxy syndrome is a rare and complex disorder of the chest and abdominal organ
arrangements, and presents a diagnostic challenge to the radiologist. This article describes
the morphological characteristics of heterotaxy and situs abnormalities, in particular left and
right atrial isomerism, and suggests an approach in evaluating the spectrum of abnormalities
associated with heterotaxy syndromes, using appropriate imaging modalities.
This article was adapted from an electronic poster entitled ‘This is the left, right?’ presented at the European Congress of Radiology in Vienna, Austria, in 2013.