Pulmonary alveolar proteinosis in a child from an informal settlement : 12 litres of fluid drained from the lungs and successful use of ECMO
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Date
Authors
White, D.A.
Klugman, S.R.
Weil, R.
Zigiriadis, E.
Green, Robin J.
Journal Title
Journal ISSN
Volume Title
Publisher
Health and Medical Publishing Group
Abstract
Pulmonary alveolar proteinosis (PAP) is a rare cause of chronic interstitial lung disease, characterised by accumulation of pulmonary
surfactant, respiratory insufficiency and an increased incidence of infections. The current standard therapy is whole-lung lavage to remove
the accumulated surfactant. We report on a cachexic 12-year-old boy from an informal settlement in South Africa, presenting for the first
time with PAP. Twelve litres of broncho-alveolar lavage fluid were drained under extracorporeal membrane oxygenation, and the patient
gained 10 kg during his 2-month admission.
Description
Keywords
Pulmonary alveolar proteinosis (PAP), Children, Informal settlements, Lung disease, 12 litres of fluid drained
Sustainable Development Goals
Citation
White, DA, Klugman, SR, Weil, R, Zigiriadis, E & Green, RJ 2013, 'Pulmonary alveolar proteinosis in a child from an informal settlement : 12 litres of fluid drained from the lungs and successful use of ECMO', South African Journal of Child Health, vol. 7, no. 4, pp. 155-157.