2025-11-272025-11-27http://hdl.handle.net/2263/106883Clinical history : An 11 year old female with pronounced hepatosplenomegaly and ascites with a liver biopsy showing post-necrotic liver cirrhosis.Autopsy findings : 1. Absence of the hepatic portal vein.2. Thrombosis of the branches of the hepatic vein.3. Chronic congestive fibrosis of the liver.4. Oesophageal varsices.5. Massive internal tract bleeding.Diagnosis: Chronic congestive fibrosis with expanded intra-hepatic thrombosis as a result of hepatic vein ostia