Unusual variant of scimitar syndrome associated with an absent right pulmonary artery, stenosis of the inferior vena cava, hemi-azygous continuation and the VACTERL association

Takawira, Farirai F.Omar, Fareed E.2013-06-262013-06-262013-05Takawira, FF & Omar, F 2013, 'Unusual variant of scimitar syndrome associated with an absent right pulmonary artery, stenosis of the inferior vena cava, hemi-azygous continuation and the VACTERL association', Cardiovascular Journal of Africa, vol. 24, no. 3, pp. e3-e6.1995-1892 (print)1680-0745 (online)10.5830/CVJA-2012-079http://hdl.handle.net/2263/21718We report on a two-month-old infant with an unusual form of scimitar syndrome, associated with an absent right pulmonary artery, obstructed inferior vena cava, hemi-azygous continuation and the VACTERL association. The infant posed a major management problem and eventually died from a lower respiratory tract infection.enCVJAScimitar syndromeAbsent pulmonary arteryHemiazygousStenosisInferior vena cavaVACTERL associationUnusual variant of scimitar syndrome associated with an absent right pulmonary artery, stenosis of the inferior vena cava, hemi-azygous continuation and the VACTERL associationArticle