Yakoob, ZarahNel, Chane2021-10-292021-10-292020-05Yakoob, Z. & Nel, C. 2020, 'Focal dermal hypoplasia - a radiographic case report', South African Dental Journal, vol. 75, no. 4, pp. 208-210.1029-4864 (print)2519-0105 (online)10.17159/2519-0105/2020/v75no4a6http://hdl.handle.net/2263/82303Focal dermal hypoplasia (FDH) is an unusual X-linked dominant disorder that affects ectoderm and mesoderm derived tissues with females affected in 90% of cases. A case report of a 12 year old female diagnosed with FDH is presented. The dental significance of these patients are multifactorial and dental management should be focused on prevention and regular monitory visits. Restoration of functionality should be addressed by a combination of orthodontic, basic restorative and prosthodontic disciplines. Due to the multisystem involvement and the dental complexities of patients suffering from FDH a multidisciplinary approach is required for optimal patient care.en© 2020 E-Doc cc. The SADJ is licensed under Creative Commons Licence CC-BY-NC-4.0.Goltz-Gorlin syndromeEctodermal dysplasiaFocal dermal hypoplasia (FDH)Article