Bellew, NeilWagener, Georg2011-03-082011-03-082011-03Bellew, N & Wagener, G 2011, 'Camurati-Engelmann disease : pictorial essay', SA Journal of Radiology, vol. 15, no. 1, pp. 20-24. [http://www.journals.co.za/sama/m_sajr.html]1027-202Xhttp://hdl.handle.net/2263/15987Camurati-Engelmann disease (CED), or progressive diaphyseal dysplasia, is a rare sclerosing dysplasia of which 250 cases have been described in the English literature. The disease affects one in a million people and is autosomal dominant with variable penetrance. It was initially described by Cockayne in 1920; Camurati was the first to suggest its hereditary nature in 1922. A single case of muscular wasting and marked bone involvement was reported by Engelmann in 1929. As the name suggests, there is progressive hyperostosis and predominant involvement of the diaphyses.enHealth & Medical Publishing GroupSteve Biko Academic Hospital (SBAH)Article