Takawira, Farirai F.Mitchell, Belinda J.Du Plessis, Dirk J.2011-08-032011-08-032010-02Takawira, FF, Mitchell, B & Du Plessis, DJ 2010, 'Unusual case of congenitally unguarded tricuspid valve orifice associated with pulmonary valve atresia and intact ventricular septum', Echocardiography, vol. 27, no. 2, pp. 202-204.0742-2822 (print)1540-8175 (online)10.1111/j.1540-8175.2009.01057.xhttp://hdl.handle.net/2263/16970We report on a premature neonate who presented with cyanosis soon after birth. She was found on echocardiography to have an unguarded tricuspid valve orifice associated with pulmonary valve atresia and an intact interventricular septum. Owing to the small-sized pulmonary arteries, she was initially managed conservatively with prostaglandin infusion, and at one year of age underwent a successful bidirectional cavo-pulmonary (Glenn) shunt operation.en© 2011 Wiley Periodicals, Inc.UnguardedTricuspid valvePulmonary valve atresiaEbstein’sCavo-pulmonaryFontanHeart valve diseases in children -- South AfricaPostprint Article