Double trouble : bilateral cerebral involvement in Sturge-Weber syndrome
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Date
Authors
Adroos, Narosha
Smal, Janet
Suleman, Farhana Ebrahim
Journal Title
Journal ISSN
Volume Title
Publisher
AOSIS OpenJournals
Abstract
Sturge-Weber syndrome, also known as encephalotrigeminal angiomatosis or meningofacial
angiomatosis, is characterised in its classical form by a congenital, usually unilateral, ‘portwine
stain’ (capillary naevus) on the face, convulsions, typical intracranial calcification and
some degree of mental retardation and hemiparesis. The clinical correlation of intractable
seizures with the presence of bilateral intracranial disease has management and prognostic
implications, thus making the presence of bilateral disease an important factor to all those
involved in the management of the child with Sturge-Weber syndrome.
Description
Keywords
Sturge-Weber syndrome, Encephalotrigeminal angiomatosis, Meningofacial angiomatosis, Portwine stain (capillary naevus), Bilateral intracranial disease, Convulsions, Intracranial calcification, Mental retardation, Hemiparesis
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Citation
Adroos N, Smal J, Suleman FE. Double trouble: Bilateral cerebral involvement in Sturge-Weber syndrome. S Afr J Rad. 2015;19(1); Art. #760, 4 pages. http://dx.DOI.org/ 10.4102/sajr.v19i1.760.