Double trouble : bilateral cerebral involvement in Sturge-Weber syndrome

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Authors

Adroos, Narosha
Smal, Janet
Suleman, Farhana Ebrahim

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AOSIS OpenJournals

Abstract

Sturge-Weber syndrome, also known as encephalotrigeminal angiomatosis or meningofacial angiomatosis, is characterised in its classical form by a congenital, usually unilateral, ‘portwine stain’ (capillary naevus) on the face, convulsions, typical intracranial calcification and some degree of mental retardation and hemiparesis. The clinical correlation of intractable seizures with the presence of bilateral intracranial disease has management and prognostic implications, thus making the presence of bilateral disease an important factor to all those involved in the management of the child with Sturge-Weber syndrome.

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Keywords

Sturge-Weber syndrome, Encephalotrigeminal angiomatosis, Meningofacial angiomatosis, Portwine stain (capillary naevus), Bilateral intracranial disease, Convulsions, Intracranial calcification, Mental retardation, Hemiparesis

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Citation

Adroos N, Smal J, Suleman FE. Double trouble: Bilateral cerebral involvement in Sturge-Weber syndrome. S Afr J Rad. 2015;19(1); Art. #760, 4 pages. http://dx.DOI.org/ 10.4102/sajr.v19i1.760.