Abstract:
Behçet’s disease is a rare, systemic variable vessel vasculitis mostly seen in patients from
the Middle East, Northern Africa and Central Asia. Neuro-Behçet disease (NBD) is often diagnosed in patients with known Behçet’s disease who present with neurological symptoms
and radiological features of central nervous system involvement. There are very few cases
with neuro-Behcet reported from Sub-Saharan Africa in the literature. We report a case of
severe parenchymal neuro-Behçet with pseudo-tumoral brainstem lesions in a young male
patient of South African origin.