Congenital infiltrating lipomatosis of the face (CILF) is a rare disorder in which overgrowth
of fatty tissue with infiltration of underlying structures leads to craniofacial deformities
and asymmetry. Imaging plays an important role in the diagnosis, surgical planning and
evaluation of underlying structures. To our knowledge, our case is the first to describe CILF
associated with isolated enlargement of a cerebellar hemisphere in the absence of an enlarged
ipsilateral cerebral hemisphere (hemimegalencephaly).